Describe the ultrashort-segment Hirschsprung disease.
Definition: very short segment of aganglionosis, limited to the distal rectum
Symptoms: less severe symptoms (e.g., chronic constipation)
Treatment: usually treated with diet and stool softeners
Prognosis: better prognosis with fewer complications
Describe the total colonic aganglionosis.
Definition: complete aganglionosis of the colon
Symptoms: ranging from incomplete intestinal obstruction to ileus
Prognosis: significant long-term morbidity and mortality (e.g., enterocolitis, post-operative bowel incontinence)
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